Describe in detail the pathophysiological process of cystic fibrosis. Describe the pathophysiology of complications of cystic fibrosis. What teaching related to her diagnosis would you provide the parents?

Describe in detail the pathophysiological process of cystic fibrosis. Describe the pathophysiology of complications of cystic fibrosis. What teaching related to her diagnosis would you provide the parents?

The Pathophysiology of Complications of Cystic Fibrosis

Cystic fibrosis affects the breathing system when the abnormal cystic fibrosis transmembrane conductance regulator protein leads to the production of the sticky mucus that blocks the airways, making it difficult for gas exchange hence leading to lungs complications and damage of lungs tissues, which eventually may lead to chronic disorders (Ghanem et al., 2020). The pathophysiology of complications of cystic fibrosis can be compound and complicated, where it germinates from the building of thick mucus in some organs. Cystic fibrosis interferes with the digestive system where the thick and sticky mucus accumulates on the pancreas, making it challenging to produce the digestive juice which is crucial in digesting proteins, hence poor nutrient absorption and stunted growth affecting even the reproductive system in men leading to infertility where cystic fibrosis can affect the respiratory system as it damages airways which makes it harder to move air in and out of the lungs and clear mucus from the bronchial tubes where the complications also affect the digestive system where the thick mucus can block the tube that carries digestive enzymes from the pancreas to the intestine increasing the risk of diabetes. such complications can be life-threatening and it is good to understand how to overcome them.

Teaching Related to the Diagnosis or the Patient

Many people are able to lead entire and active lives due to proper care and management. For the Caucasian female diagnosed with the disorder, it would be necessary for her parents to understand that the condition of their child requires regular care and management, the parents will have to work closely with their child’s healthcare team to come up with a treatment plan that addresses the child’s specific needs and it may include medications such as antibiotics and bronchodilators and also therapies to help remove mucus from the lungs and the digestive tract (Collins, 2018). The parents would also be needed to give attention to their child’s nutritional needs because cystic fibrosis affects the body’s way of absorbing nutrients. When the parents follow the above teaching, it will enable their daughter to live a joyful life without much complication. The child may live for a long time with the disorder but with fewer complications after proper care and management.

Conclusion

Cystic fibrosis is a genetic disorder that damages the lungs, digestive system, and other organs in the body and it affects the cells that produce mucus, sweat, and digestive juices, pathophysiological process of fibrosis is about the abnormal functioning of cystic fibrosis transmembrane conductance regulator protein, where a thick mucus builds up in some body organs, leading to a harmful health condition. Pathophysiology of complications of cystic fibrosis can be compound and complicated, where it develops from the building of thick mucus in some organs. It would be necessary for the child’s parents to understand that the condition of their child requires regular care and management and they have to work closely with their child’s healthcare team to come up with a treatment plan that addresses the child’s specific needs.

References

Bell, S. C., Mall, M. A., Gutierrez, H., Macek, M., Madge, S., Davies, J. C., … & Ratjen, F. (2020). The future of cystic fibrosis care: a global perspective. The Lancet Respiratory Medicine, 8(1), 65-124. https://doi.org/10.1016/S2213-2600(19)30337-6

Collins, S. (2018). Nutritional management of cystic fibrosis–an update for the 21st century. Paediatric respiratory reviews, 26, 4-6. https://doi.org/10.1016/j.prrv.2017.03.006